| Título: | Rett Syndrome: a challenge to an anaesthetist |
| Autores: |
Maheshwari, Namrata; Assistant Professor, Dept of Anaesthesiology, Sir Grant Medical College Gandhi, Deepak; JJ Hospital, Mumbai |
| Fecha: | 2012-04-21 |
| Publicador: | Sri Lankan journal of Anaesthesiology |
| Fuente: |
 |
| Tipo: |
info:eu-repo/semantics/article Peer-Reviewed Item info:eu-repo/semantics/publishedVersion |
| Tema: |
Anaesthesiology Rett’s Syndrome; regional anaesthesia,; scoliosis |
| Descripción: | Rett syndrome is a progressive neurological disorder of females characterized by dementia, severe autism, movement disorders, growth retardation, microcephaly, seizures, muscle wasting, scoliosis and an abnormality of respiratory control 1 .These patients may show a characteristic abnormal respiratory pattern consisting of episodes of tachypnea and irregular respiration, intermixed with apnoea, observed only during wakefulness.2 Anaesthesia is challenging in this rare subgroup of patients with its multiple comorbid presentations. This report provides a practical approach comprising of vigilant monitoring and proactive actions like preoperative oxygenation, anti-epileptic medications, adequate fluid infusion and unilateral spinal anaesthesia restricting level to T 10 to avoid respiratory distress for anaesthesia in a patient with Rett syndrome for sub trochanteric fracture nailing.DOI: http://dx.doi.org/10.4038/slja.v20i1.4275 Sri Lankan Journal of Anaesthesiology 20(1): 53-55 (2012) |
| Idioma: | Inglés |
1 A National Resuscitation Council por Hapuarachchi, Shirani; Consultant Anaesthetist , Neuro Surgical Department, The National Hospital of Sri Lanka | 6 Surviving severe sepsis – early recognition and treatment por Khan, Fazal Hameed; Professor, Department of Anaesthesia, Akuh, Karachi |
2 Theatre efficiency por Abayadeera, Anuja; Senior Lecturer in Anaesthesiology Faculty of Medicine, University of Colombo | 7 Stabilization and transport of head injured por Kularatne, Manjula; Consultant Anaesthetist, Teaching Hospital Colombo South |
3 Use of phenylephrine as vasopressor of choice to prevent hypotension following spinal anaesthesia in LSCS por Pinto, V; Consultant Anaesthetist, Senior lecturer, Department of Anesthesiology, Faculty of Medicine, University of Peradeniya,Jaysundara, NS; Temporary Lecturers, Department of Anesthesiology, Faculty of Medicine University of Peradeniya,Abeysundara, AB; Registrar in Anesthesiology, General Hospital Kandy,Ekanayake, SU; Temporary Lecturers, Department of Anesthesiology, Faculty of Medicine University of Peradeniya, Sri Lanka | 8 Quality assurance in critical care por Hoda, Muhammad Qamarul; Professor, Department of Anaesthesia, Aga Khan University, Karachi |
4 Fainting attacks on the dental chair: "functional" or RAS? por Nageswaran, H; Foundation Year 2, Luton and Dunstable Foundation Trust, Lewsey Road, Luton, UK,Peiris, T Malathie; Consultant Anaesthetist, Luton and Dunstable Foundation Trust, Lewsey Road, Luton | 9 Ventilatory strategies in chronic obstructive pulmonary disease por Habaragamuwa, BWP; Senior Registrar in Anaesthesiology, The National Hospital |
5 Critical care management of head injury – current concepts por Hoda, Muhammad Qamarul; Professor and Clinical Director ICU Aga Khan University, Karachi | 10 Haemorrhage and coagulation a practical approach por Lyons, Gordon; Consultant Obstetric Anaesthetist St James’ University Hospital, Leeds, United Kingdom |